|
KMID : 1103720140700010255
|
|
Journal of the Korean Society of Radiology
2014 Volume.70 No. 1 p.255 ~ p.259
|
|
|
Idiopathic Pleuroparenchymal Fibroelastosis, a Rare Entity of Interstitial Pneumonia: A Case Report
|
|
Park Jong-Chun
Chae Eun-Jin
Song Joon-Seon
|
|
|
Abstract
|
|
|
|
Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a recently described, very rare type of fibrotic interstitial lung disease predominantly involving subpleural areas of both upper lungs. IPPFE has distinctive radiologic and pathologic features: progressive subpleural opacity with fibrotic changes, predominantly in upper lungs, and dense elastic component on histology. We experienced one case of surgically confirmed IPPFE, with progression of radiologic findings on the serial CT examinations. We herein report the characteristic radiologic features of IPPFE with pathologic and clinical manifestations.
|
|
|
KEYWORD
|
|
|
Idiopathic Pleuroparenchymal Fibroelastosis, Interstitial Lung Disease, Upper Lobe Fibrosis, Lung
|
|
|
FullTexts / Linksout information
|
|
|
|
|
|
Listed journal information
|
|
  
|